A Case of Cardiac Amyloidosis with Complete Atrioventricular Conduction Block Treated by Permanent Pacemaker.
10.4070/kcj.1996.26.5.1058
- Author:
Seung Won JIN
;
Ho Joong YOUN
;
Sang Hyun LIM
;
Yung Whan KIM
;
Jong Hyun YOUN
;
Hee Kyung CHUN
;
Wook Sung CHUNG
;
Jae Hyung KIM
;
Kyu Bo CHOI
;
Soon Jo HONG
;
Kyo Young LEE
;
Sang In SHIM
- Publication Type:Case Report
- Keywords:
Cardiac amyloidosis;
Complete atrioventricular block;
Permanent pacemaker
- MeSH:
Amyloidosis*;
Atrioventricular Block*;
Biopsy;
Echocardiography;
Electrocardiography;
Eosinophils;
Female;
Heart;
Humans;
Korea;
Lighting;
Middle Aged;
Myocytes, Cardiac
- From:Korean Circulation Journal
1996;26(5):1058-1067
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
In generalized amyloidosis, involvement of heart is not rare, but development fo severe conduction distubance in cardiac amyloidosis is a rare presentation in a clinical situation. We report the first case in Korea of cardiac amyloidosis with complete atrioventricular block, which was confirmed by endomyocardial biopsy. A 59-year-old woman was admitted due to drowsy mentality. We observed a severe atrioventricular conduction disturbance on the electrocardiogram and a marked hypertrophied ventricular wall and a granular sparkling appearance within the wall, a characteristic feature in cardiac infiltration of amyloidosis, on the echocardiography. Endomyocardial biopsy was performed and revealed extensive deposition of amorphous eosinophilic materials within the cardiac muscle cells. Polarizing illumination after Congo-red staining showed typical green birefrigence. We performed a insertion of permanent pacemaker(VVI type) for the treatment of complete atrioventricular block.
