Cancer Development in the Remained Rectum after Subtotal Colectomy in a Familial Adenomatous Polyposis Patient.
- Author:
Dae Sik LIM
;
Seung Ho CHOI
;
Byung Kwon AHN
;
Sung Uhn BAEK
- Publication Type:Original Article
- Keywords:
FAP;
Remained rectum;
Malignancy
- MeSH:
Abdominal Pain;
Adenomatous Polyposis Coli*;
Adenomatous Polyps;
Colectomy*;
Colon;
Diarrhea;
Humans;
Ileostomy;
Incidence;
Mucous Membrane;
Postoperative Complications;
Proctocolectomy, Restorative;
Rectum*
- From:Journal of the Korean Society of Coloproctology
1998;14(3):635-642
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Familial adenomatous polyposis (FAP) is an hereditary autosomal dominant disease characterized by development of hundreds to thousands of adenomatous polyps in the colon and rectum. The common symptoms are bloody stool, diarrhea, and abdominal pain. The average age at onset of symptoms is 33 years. Because of inevitable progression to malignancy, it is necessary to remove the entire colonic and rectal mucosa. Current surgical options are total proctocolectomy with permanent ileostomy, trans-abdominal colectomy with ileorectal anastomosis (IRA), and restorative proctocolectomy with ileal pouch-anal anastomosis (IPAA). Recently IPAA can give optimum control of colorectal polyposis in FAP patients with an acceptable incidence of postoperative complications and satisfactory functional results. We experienced one case of FAP who had malignacy in the remained rectum after subtotal colectomy. IPAA was done and the result was satisfactory.