A Case of External Auditory Canal Stenosis in Langerhans Cell Histiocytosis.
- Author:
Inkyung SOHN
1
;
Han Bin LEE
;
Sung Yeul KIM
;
Yun Hoon CHOUNG
Author Information
1. Department of Otolaryngology, Ajou University School of Medicine, Suwon, Korea. yhc@ajou.ac.kr
- Publication Type:Case Report
- Keywords:
Langerhans cell histiocytosis;
Temporal bone;
External auditory canal;
Stenosis
- MeSH:
Adult;
Bone Marrow;
Constriction, Pathologic;
Ear Canal;
Eosinophilic Granuloma;
Histiocytes;
Histiocytosis, Langerhans-Cell;
Humans;
Liver;
Lung;
Lymph Nodes;
Male;
Mononuclear Phagocyte System;
Skin;
Spleen;
Temporal Bone
- From:Korean Journal of Audiology
2011;15(2):90-93
- CountryRepublic of Korea
- Language:English
-
Abstract:
Langerhans cell histiocytosis (LCH) refers a group of disorders of the reticuloendothelial system characterized by a proliferation of histiocytes, which includes eosinophilic granuloma, Lettere-Siwe diseases, and Hand-Schuler Christian disease. The clinical presentation of LCH depends on the site of involvement. It can range from multifocal lesions to a solitary lesion. Tissues characteristically involved in LCH are bone, skin, lung, liver, spleen, bone marrow, lymph nodes and the hypothalamic-pituitary region, although the involvement of other organs such as the bowel can occur. We experienced a case of external auditory canal stenosis in LCH of multiple organ involvement in a 28-year-old male, and report it with a review of the relevant literature.