Catastrophic Primary Antiphospholipid Syndrome.
10.3348/jkrs.2006.55.3.263
- Author:
Dong Hun KIM
1
;
Joo Nam BYUN
;
Sang Wan RYU
Author Information
1. Department of Radiology, Chosun University Hospital, Korea. kdhoon@chosun.ac.kr
- Publication Type:Case Report
- Keywords:
Antiphopholipid syndrome;
Pulmonary arteries, thrombosis;
Intestines, infarction
- MeSH:
Antibodies, Anticardiolipin;
Anticoagulants;
Antiphospholipid Syndrome*;
Cholecystectomy;
Dyspnea;
Humans;
Infarction;
Male;
Mesenteric Artery, Superior;
Middle Aged;
Necrosis;
Pulmonary Embolism;
Respiratory Distress Syndrome, Adult;
Steroids;
Thrombosis;
Urinary Bladder
- From:Journal of the Korean Radiological Society
2006;55(3):263-266
- CountryRepublic of Korea
- Language:English
-
Abstract:
Catastrophic antiphospholipid syndrome (CAPLS) was diagnosed in a 64-year-old male who was admitted to our hospital with dyspnea. The clinical and radiological examinations showed pulmonary thromboembolism, and so thromboembolectomy was performed. Abdominal distention rapidly developed several days later, and the abdominal computed tomography (CT) abdominal scan revealed thrombus within the superior mesenteric artery with small bowel and gall bladder distension. Cholecystectomy and jejunoileostomy were performed, and gall bladder necrosis and small bowel infarction were confirmed. The anticardiolipin antibody was positive. Anticoagulant agents and steroids were administered, but the patient expired 4 weeks after surgery due to acute respiratory distress syndrome (ARDS). We report here on a case of catastrophic APLS with manifestations of pulmonary thromboembolism, rapidly progressing GB necrosis and bowel infarction.
