Cor Triatriatum with Infracardiac Total Anomalous Pulmonary Venous Drainage.
- Author:
Man Jong BAEK
1
;
Woong Han KIM
;
Chan Young NA
;
Sam Se OH
;
Soo Cheol KIM
;
Jae young LEE
;
Yang Bin JEON
;
Seog Ki LEE
;
Chang Ha LEE
;
Jae Woong LEE
;
Wook Sung KIM
;
Young Tak LEE
;
Young Kwang PARK
;
Chong Whan KIM
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute, Puchon-shi, Kyonggi-do, Korea. woonghan@korea.com
- Publication Type:Case Report
- Keywords:
Cor triatriatum;
Pulmonary vein, total anomalous return
- MeSH:
Constriction, Pathologic;
Cor Triatriatum*;
Cyanosis;
Diagnosis;
Drainage*;
Echocardiography;
Female;
Heart;
Humans;
Membranes;
Mitral Valve Insufficiency;
Pulmonary Veins
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2002;35(1):52-55
- CountryRepublic of Korea
- Language:English
-
Abstract:
We report one case of an 18-day-old female patient, weighing 3.4 kg, with severe cyanosis. The diagnosis was made with only transthoracic echocardiography, which revealed cor triatriatum with an atretic small opening of fibromuscular membrane, obstructive infracardiac total anomalous pulmonary venous drainage(TAPVD), severely restrictive interatrial communication, and scanty mitral inflow and aortic forward flow. The preoperative decision-making for biventricular repair was not easy due to collapsed left heart system caused by remarkably reduced blood flow. An emergent operation was performed due to severe cyanosis. All left heart structures were somewhat hypoplastic but thought to be adequate for systemic circulation. Biventricular repair was done without specific intraoperative problems. The postoperative course was uneventful. The patient has been doing well with no evidence of pulmonary vein stenosis or mitral regurgitation for 4 months after operation.
