Primary intimal saroma of the aorta.
- Author:
In Ho CHAE
1
;
Dae Won SOHN
;
Young Bae PARK
;
Young Woo LEE
;
Yoon Seok CHANG
;
Moo Yong RHEE
Author Information
1. Department of Internal Medicine, Seoul National University College of Medicine, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Aorta;
Sarcoma;
Transesophageal echocardiography
- MeSH:
Abdominal Pain;
Actins;
Adult;
Angiography;
Aorta*;
Autopsy;
Biopsy;
Diagnosis, Differential;
Early Diagnosis;
Echocardiography;
Echocardiography, Transesophageal;
Female;
Flank Pain;
Hemorrhage;
Humans;
Intestine, Small;
Kidney;
Neoplasm Metastasis;
Ovary;
Prognosis;
Rare Diseases;
Sarcoma;
Thrombosis;
Vimentin
- From:Korean Journal of Medicine
1999;57(5):950-955
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Primary intimal sarcoma of the aorta is a rare disease and has poor prognosis due to the difficulty of early diagnosis. Recently, we experienced a 42 year-old female patient who had primary intimal sarcoma of the aorta with metastasis. She complained of claudication, abdominal pain, flank pain and pulselessness. CT angiography showed thrombus-like lesion in the aorta. In our case, the transesophageal echocardiographic findings were different from those of usual thrombus, which suggested the importance of transesophageal echocardiography in the differential diagnosis of intra-aortic mass. Exploration was done because of the highly mobile portion and the biopsy revealed that the mass was intimal sarcoma. Immunohistochemical staining for actin and vimentin was positive. She died of massive gastrointestinal bleeding during admission. At autopsy, the sarcoma was found to metastasize into small intestine, kidney, and ovary.
