Four Cases of Phakomatosis Pigmentovascularis.
- Author:
Jai Il YOUN
;
Gwang Yeol JOH
;
Ai Young LEE
;
Yoo Shin LEE
- Publication Type:Case Report
- Keywords:
Phakomatosis pigmentovascularis;
Dermal melanocytosis;
Nevs flammeus
- MeSH:
Hypertrophy;
Mongolian Spot;
Neurocutaneous Syndromes*;
Nevus of Ota;
Port-Wine Stain;
Seizures
- From:Korean Journal of Dermatology
1985;23(1):112-119
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Dermal melanocytosis such as nevus of Ota and extensive Mongolian spots are sometimes associated with hemangiomatous changes. Ota gave the designation of phakorriatosis pigmentovascularis to a spectrum of these combinations. We oLserved four cases of phakomatosis pigmentovascularis. They showed extensive, various dermal melanocytosis and widespread nevus flammeus. They exhibited signs of involvement of the systemic organs such as abnormality of electroencephalograrn, soft tissue hypertrophy and convulsion.
