Experience of Benign Multiple Symmetrical Lipomatosis.
- Author:
Chul HUH
1
;
Goo Hyun MUN
;
Soo Hyang LEE
;
Hyung Joon KIM
;
So Young LIM
;
Won Sok HYON
;
Sa Ik BANG
;
Kap Sung OH
Author Information
1. Samsung Medical Center, Department of Plastic Surgery, Sungkyunkwan University School of Medicine, Seoul, Korea. gh.mun@samsung.com
- Publication Type:Case Report
- Keywords:
Lipomatosis;
Madelung's disease
- MeSH:
Arm;
Dyspnea;
Humans;
Lipectomy;
Lipomatosis;
Lipomatosis, Multiple Symmetrical*;
Neck;
Recurrence;
Shoulder;
Sleep Apnea Syndromes
- From:Journal of the Korean Cleft Palate-Craniofacial Association
2007;8(1):29-32
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Benign symmetrical lipomatosis, also known as Madelung's disease, is a rare condition characterized by massive fatty deposits arranged symmetrically around the neck, shoulders, and arms. Patients usually complain of their cosmetic appearance, but treatment can be considered for decreased neck motion and/or aerodigestive problems. Surgical lipectomy and liposuction are treatment of choice, but recurrence is common. Because the distribution of the lesion tends to be wide and diffuse, single operation is not sufficient for improving contour and functional problems, especially in severely affected case. We experienced a progressed patient who suffered from limitation of neck motion, dyspnea including sleep apnea due to massive deposits on whole neck. We performed 2 staged operations for the purpose of removing as much lipomatous tissue as possible. After 2 staged excisions, patient's appearance and aerodigestive problems are much improved and recurrence is not observed.
