A Cases of Adult Onset Still's Disease with Hemolytic Anemia.
10.4078/jrd.2012.19.2.104
- Author:
Jin Kyu JUNG
1
;
Yong Jun KIM
;
Chang Kyoo BYON
;
Sang Yeob LEE
;
Sung Won LEE
;
Won Tae CHUNG
Author Information
1. Department of Internal Medicine, College of Medicine, Dong-A University, Pusan, Korea. wtchung@dau.ac.kr
- Publication Type:Case Report
- Keywords:
Adult onset still disease;
Hemolytic anemia
- MeSH:
Adult;
Anemia, Hemolytic;
Arthralgia;
Disseminated Intravascular Coagulation;
Exanthema;
Fever;
Humans;
Leukocytosis;
Liver;
Lymphohistiocytosis, Hemophagocytic;
Still's Disease, Adult-Onset
- From:Journal of Rheumatic Diseases
2012;19(2):104-107
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Adult onset Still's disease (AOSD) is a systemic inflammatory disorder of unknown etiology. AOSD is characterized by fever, arthralgia, salmon-colored skin rash, hepatosplenomegaly and its laboratory abnormalities include leukocytosis, elevated liver enzyme, negative autoantibody, and hyperferritinemia. The clinical course varied and severe complicated conditions, such as hemophagocytic syndrome, and disseminated intravascular coagulation, occurred occasionally. Such a complication is accompanied with hemolytic anemia and lead to be a fatal course. We report the first case of AOSD with hemolytic anemia, which improved with high dose steroid therapy.
