A Communicating Bronchopulmonary Foregut Malformation Associated with Absence of the Left Pericardium: A case report.
- Author:
Dong Gon YOO
1
;
Chong Wook KIM
;
Chong Bin PARK
;
Pil Je KANG
;
Jong Hyeog LEE
Author Information
1. Department of Thoracic & Cardiovascular Surgery, Gangneung Asan Hospital, University of Ulsan College of Medicine. jokim@ghah.co.kr
- Publication Type:Case Report
- Keywords:
Esophageal congenital anomalies;
Lung anomaly;
Pericardium
- MeSH:
Angiography;
Bronchogenic Cyst;
Bronchography;
Bronchopulmonary Sequestration;
Esophagus;
Fistula;
Lung;
Magnetic Resonance Imaging;
Pericardium*;
Pneumonia;
Prognosis;
Stomach
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2007;40(11):793-797
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A communicating bronchopulmonary foregut malformation (CBPFM) is a rare congenital anomaly that is characterized by a fistula between isolated respiratory tissue and the esophagus or stomach. The presence of accessory lung tissue arising from the primitive gastrointestinal tube is a common factor in the development of all forms of bronchopulmonary foregut malformations. Recurrent pneumonia associated with cystic radiographic structures is a characteristic of the condition. Further imaging studies using esophagogram, bronchography, computerized tomography, MRI, and arteriography can help in making a diagnostic evaluation. The treatment is a surgical resection of the involved lung tissue, and fistula closure with a good prognosis. We encountered a case of CBPFM, who presented with an extralobar pulmonary sequestration and bronchogenic cyst communicating with a tubular esophageal duplication that was associated with a complete left pericardial defect.
