Perirenal Lymphangiomatosis.
10.5534/wjmh.2014.32.2.116
- Author:
Tae Gyeong JEON
1
;
Do Hoon KONG
;
Hyun Jun PARK
;
Suk KIM
;
Won Young PARK
;
Soo Dong KIM
;
Hong Koo HA
Author Information
1. Department of Urology, Pusan National University Hospital, Busan, Korea. hongkooha@naver.com
- Publication Type:Case Report
- Keywords:
Kidney;
Lymphangioma;
Lymphatic diseases;
Neoplasms
- MeSH:
Adult;
Dilatation;
Drainage;
Flank Pain;
Humans;
Kidney;
Lymphangioma;
Lymphatic Diseases;
Nephrectomy;
Pleural Effusion
- From:The World Journal of Men's Health
2014;32(2):116-119
- CountryRepublic of Korea
- Language:English
-
Abstract:
Lymphangioma is a rare, benign mesenchymal neoplasm, which is characterized by numerous intercommunicating cystic spaces containing lymphatic fluid. It is considered a congenital disease resulting from the obstruction of regional lymph drainage during the developmental period. Lymphangioma may be focal/unilateral or diffuse/bilateral, and in the latter case, it is referred to as lymphangiomatosis. Here, we report a case of a 38-year-old man with perirenal lymphangiomatosis. The patient's chief complaint was left flank pain, and left pleural effusion was found on radiological examination. After radical nephrectomy, the pathological examinations revealed that the kidney was enclosed by a multicystic mass with intrarenal cystic dilatations. We report the case and discuss the management of perirenal lymphangiomatosis with a literature review.