Mazabraud's Syndrome: A case report.
- Author:
Jeong Geun HONG
1
;
Jin Soo LIM
;
Ho KWON
;
Sang Hoon CHUNG
Author Information
1. Department of Plastic Surgery, College of Medicine, The Catholic University of Korea.
- Publication Type:Case Report
- Keywords:
Mazabrauds syndrome;
Fibrous dysplasia;
Intramuscular myxoma
- MeSH:
Clavicle;
Fibrous Dysplasia of Bone;
Fibrous Dysplasia, Polyostotic;
Forearm;
Myxoma;
Radionuclide Imaging;
Radius;
Scapula;
Skull;
Tomography, X-Ray Computed
- From:Journal of the Korean Society of Plastic and Reconstructive Surgeons
2000;27(2):176-178
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Mazabraud's syndrome is rare benign disease characterized by the association of intramuscular myxoma and fibrous dysplasia of bone. We present a case of multiple intramuscular myxomas of the right forearm with polyostotic fibrous dysplasia. X-rays suggested fibrous dysplasia of adjacent bones and CT scans showed two intramuscular cystic masses on the right forearm. 99mTc bone scintigraphy also showed a markedly increased uptake in the skull, both scapulas, both clavicles and both humeri. The masses were successfully removed. Fibrous dysplasia of the radius and myxoma were confirmed by pathologic study.
