Primitive Neuroectodermal Tumor of the Liver in a 13-year-old Boy: A Case Report.
- Author:
Sang Goo LEE
1
;
Ji Eun KIM
;
Ji Hyuk LEE
;
Hye Jin LEE
;
Jong Seung LEE
;
Jee Hyun LEE
;
Yon Ho CHOE
Author Information
1. Department of Pediatrics, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea. i101016@skku.edu
- Publication Type:Case Report
- Keywords:
Liver;
PNET
- MeSH:
Abdominal Pain;
Adolescent;
Biopsy;
Diagnosis, Differential;
Fever;
Granuloma, Plasma Cell;
Humans;
Immunohistochemistry;
Liver;
Neuroectodermal Tumors, Primitive;
Prognosis;
Rare Diseases
- From:Korean Journal of Pediatric Gastroenterology and Nutrition
2008;11(2):214-218
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Primary primitive neuroectodermal tumor (PNET) of the liver is a rare disease with aggressive behavior and poor prognosis. We report a case of a PNET of the liver in a 13-year-old boy. The patient was admitted to the hospital with fever and abdominal pain. Abdominal CT and MRI revealed a 5.5 cm sized, septated, non-enhancing mass in the hepatic hilum. The patient was initially diagnosed with an inflammatory pseudotumor. Despite 9 days of antibiotic therapy, the patient's clinical symptoms did not improve. A liver biopsy was performed in the interest of formulating a differential diagnosis. This procedure revealed tumor cells positive for CD99 on immunohistochemistry. The patient was diagnosed with a PNET.
