Successful Removal of Left Ventricular Rhabdomyoma : A Rare Cause of Left Ventricular Outflow Obstruction in the Newborn Infant: 1 case report.
- Author:
Byoung Hee AHN
1
;
Hyeong Sun MOON
;
Kook Joo NA
;
Sang Hyung KIM
;
Byung Ju KIM
;
Jae Sook MA
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Chonnam University Medical School, Korea.
- Publication Type:Case Report
- Keywords:
Ventricular outflow tract obstruction, left;
Heart neoplasm;
Infant;
Rhabdomyoma;
Echocardiography
- MeSH:
Cardiopulmonary Bypass;
Constriction, Pathologic;
Cyanosis;
Echocardiography;
Female;
Heart Neoplasms;
Humans;
Infant;
Infant, Newborn*;
Prognosis;
Rhabdomyoma*;
Tachypnea;
Tuberous Sclerosis;
Ventricular Outflow Obstruction*
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
1997;30(2):205-208
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Cardiac rhabdomyomas are the most common primary tumor in infancy and childhood and are frequently associated with tuberous sclerosis. Although spontaneous regression of cardiac rhabdomyoma has been reported , prognosis of this tumor associated with subaortic stenosis is still considered to be poor and surgery continues to be indicated. A 4-day-old female was admitted due to tachypnea and cyanosis. Single rhabdomyoma arising from the interventricular septum associated with severe subaortic stenosis was partially removed under cardiopulmonary bypass. Excised tumor size was 0.7 X 0.9 X 0.4 cm in dimension. The postoperative course was uneventful and the infant discharged on the 14th postoperative day.
