Pedunculated Nodules as a Variant of Dermatofibrosarcoma Protuberans.
- Author:
Min Jung KIM
1
;
Min Seok HUR
;
Byung Gon CHOI
;
Soo Young KIM
;
Yang Won LEE
;
Yong Beom CHOE
;
Kyu Joong AHN
Author Information
- Publication Type:Case Report
- Keywords: Dermatofibrosarcoma protuberans; Multiple pedunculated nodules
- MeSH: Adult; Dermatofibrosarcoma*; Diagnosis; Fibroblasts; Follow-Up Studies; Humans; Middle Aged; Neoplasm Metastasis; Rare Diseases; Recurrence; Sarcoma; Skin; Transplants
- From:Annals of Dermatology 2016;28(5):629-631
- CountryRepublic of Korea
- Language:English
- Abstract: Dermatofibrosarcoma protuberans (DFSP) is a rare disease of dermal fibroblastic origin that accounts for less than 5% of all soft tissue sarcomas in adults. DFSP grows slowly and is an asymptomatic lesion at the initial diagnosis. Herein, we report a case of multiple pedunculated nodules as a variant of DFSP. A 47-year-old man presented with a 7-month history of multiple well-circumscribed, firm, pedunculated nodules on the inguinal area. Histopathologic examination results showed densely packed uniform spindle cells with a storiform and cartwheel pattern, and positivity for CD34. Wide excision and skin graft were performed and at the 6-month follow-up, there was no evidence of recurrence or metastasis.
