Caroli's disease misdiagnosed as intraductal papillary neoplasm of the bile duct.
10.3350/cmh.2015.21.2.175
- Author:
Dae Hoe GU
1
;
Min Seon PARK
;
Chang Ho JUNG
;
Yang Jae YOO
;
Jae Young CHO
;
Yun Ho LEE
;
Yeon Seok SEO
;
Hyung Joon YIM
;
Soon Ho UM
;
Ho Sang RYU
Author Information
1. Department of Internal Medicine, Korea University College of Medicine, Seoul, Korea. drseo@korea.ac.kr
- Publication Type:Case Reports
- Keywords:
Caroli's disease;
Intraductal papillary neoplasm of the bile duct;
Segmentectomy
- MeSH:
Adult;
Bile Duct Neoplasms/diagnosis/pathology;
Bile Ducts, Intrahepatic;
Caroli Disease/*diagnosis/pathology;
Diagnostic Errors;
Humans;
Magnetic Resonance Imaging;
Male;
Tomography, X-Ray Computed
- From:Clinical and Molecular Hepatology
2015;21(2):175-179
- CountryRepublic of Korea
- Language:English
-
Abstract:
Caroli's disease is a rare autosomal-recessive disorder caused by malformation of the ductal plate during embryonic development. Although it is present at birth, Caroli's disease is typically not diagnosed until between the second and fourth decades of life, as it was in the present patient. Here we report a rare case of Caroli's disease limited to one liver segment, which was initially misdiagnosed as an intraductal papillary neoplasm of the bile duct. The asymptomatic patient was treated with liver segmentectomy.
