Diffuse Ganglioneuromatosis of Appendix associated with Von Recklinghausen;s Disease.
- Author:
Young Su KIM
1
;
Sang Chul NAM
;
Man Hoon HAN
;
Jeong Shik KIM
;
Ji Yun JEONG
;
Han Ik BAE
Author Information
1. Department of Pathology, Kyungpook National University School of Medicine, Daegu, Korea. baehi@knu.ac.kr
- Publication Type:Case Report
- Keywords:
Ganglioneuromatosis;
Appendix;
Von Recklinghausen's disease
- MeSH:
Appendix*;
Colon;
Ileum;
Multiple Endocrine Neoplasia;
Neurofibroma, Plexiform;
Neurofibromatosis 1
- From:Korean Journal of Pathology
2007;41(5):334-336
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Gastrointestinal ganglioneuromatosis is a rare neoplastic condition that can occur in association with von Recklinghausen's disease with multiple endocrine neoplasia type II B. The main locations are the ileum, colon, and appendix. We report a case of diffuse ganglioneuromatosis of the appendix associated with a mesenteric and ileocecal plexiform neurofibroma in von Recklinghausen's disease.
