A Case of Fulminant Bronchiolitis Obliterans Organizing Pneumonia.
10.4046/trd.1998.45.1.204
- Author:
Mi Seon KIM
1
;
Jung Hyun CHANG
;
Tai Hee KIM
;
Ju Hyun CHA
;
Hae Young KIM
;
Sun Hee SUNG
Author Information
1. Department of Internal Medicine, College of Medicine, Ewha Womans University, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Rapidly progressive bronchiolitis obliterans organizing pneumonia
- MeSH:
Adult;
Biopsy;
Bronchioles;
Bronchiolitis Obliterans*;
Bronchiolitis*;
Cough;
Cryptogenic Organizing Pneumonia*;
Dyspnea;
Fibrosis;
Humans;
Lung;
Lung Diseases, Interstitial;
Prognosis;
Weight Loss
- From:Tuberculosis and Respiratory Diseases
1998;45(1):204-212
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Bronchiolitis obliterans organizing pneumonia(BOOP) is a type of diffuse interstitial lung disease that has emerged in the past decade as an important cause of acute respiratory illness in adult. Clinically, the entity usually starts with a subacute influenza-like illness, followed by cough, progressive dyspnea, and weight loss. Organized inflammatory polypoid materials predominantly affecting distal bronchioles, alveolar ducts, and peribronchial alveolar spaces are a key pathologic findings. BOOP is characterized by a good response to glucocorticoid and an excellent prognosis. However, there is a subset of BOOP who presents with a fulminant course leading to death or chronic severe fibrosis with marked impairment of lung function. Recently, we have experienced a case of rapidly progressive BOOP, diagnosed by open lung biopsy and showed a reluctant response to corticosteroid.