A Case of Primary Intestinal Lymphangiectasia.
- Author:
Dae Hwan HWANG
1
;
Jung Woo HAN
;
Ji Hong KIM
;
Seok Joo HAN
;
Soon Won HONG
Author Information
1. Department of Pediatrics, Yonsei University College of Medicine, Seoul, Korea. KKKJHD@yumc.yonsei.ac.kr
- Publication Type:Case Report
- Keywords:
Primary intestinal lymphangiectasia;
Protein losing enteropathy
- MeSH:
Child;
Diarrhea;
Diet;
Edema;
Humans;
Hypoalbuminemia;
Intestines;
Lymphocytes;
Male;
Peritoneum;
Protein-Losing Enteropathies;
Triglycerides
- From:Korean Journal of Pediatric Gastroenterology and Nutrition
2004;7(2):253-259
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Primary intestinal lymphangiectasia is a congenital lymphatic disorder in which intestinal lymphatic channels are dilated and ruptured resulting in loss of protein, lipid, and lymphocyte into the intestine or peritoneum. As a result, hypoalbuminemia, generalized edema, diarrhea are clinically manifested. We report a case of primary intestinal lymphangiectasia with generalized edema which occurred in a 7-year old boy who was treated with lipid restriction diet with medium chain triglyceride oil supplement.
