Prolonged Survival of an Adult with Hydranencephaly.
- Author:
Jong Seok BAE
1
;
Sang Jin KIM
;
Kang Min PARK
;
Geun Ha CHI
;
Tae Gyu HWANG
Author Information
1. Department of Pediatrics, College of Medicine, Inje University, Busan, Korea. htg6700@chol.com
- Publication Type:Case Report
- Keywords:
Hydranencephaly;
Survival;
Prolonged;
Adult
- MeSH:
Adult*;
Cerebrospinal Fluid;
Cerebrum;
Child;
Humans;
Hydranencephaly*;
Prognosis
- From:
Journal of the Korean Child Neurology Society
2007;15(2):216-219
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Hydranencephaly is a rare condition in which the brain's cerebral hemispheres are absent and replaced by sacs filled with cerebrospinal fluid. The prognosis for children with hydranencephaly is generally poor, so many children with this disorder die before the age of 1 year. We experienced a patient with hydranencephaly who showed prolonged survival until age of 22 years. To our limited knowledge, this case may be the longest survival of a patient with hydranencephaly in the world.
