A Case of Satoyoshi Syndrome Presented with Progressive Muscular Spasm and Alopecia.
- Author:
Kyung Ran SON
1
;
Jin Hwa KOOK
;
Byung Ju KIM
;
Sung Jin KIM
;
Jae Sook MA
Author Information
1. Department of Pediatrics, Chonnam National University Medical School, Gwangju, Korea. kimbj@chonnam.ac.kr
- Publication Type:Case Report
- Keywords:
Satoyoshi syndrome;
Muscle spasm;
Alopecia
- MeSH:
Adolescent;
Alopecia*;
Amenorrhea;
Autoimmunity;
Child;
Diarrhea;
Female;
Humans;
Muscle Cramp;
Prednisolone;
Scalp;
Spasm*
- From:Journal of the Korean Pediatric Society
2002;45(9):1165-1169
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Satoyoshi syndrome(generalized Komuragaeri disease) is a rare disorder of unknown cause, characterized by progressive, painful, intermittent muscle spasms and alopecia. Endocrinopathy with amenorrhea, secondary skeletal abnormalities, and diarrhea or unusual malabsorption are frequently seen. It seems that autoimmunity may play a role in its pathogenesis. We report a 13-year-old girl with characteristic manifestations of the syndrome. She was treated with intravenous gammaglobulin and Prednisolone. Painful muscle cramps were gradually improved, but the scalp condition did not change. Satoyoshi syndrome should be considered in children with unexplained muscle spasms and alopecia.
