Postnatal Left Ventricular Outflow Tract Obstruction Caused by Multiple Rhabdomyoma Tumors.
- Author:
Seunghwan SONG
1
;
Tae Gook JUN
;
Min Suk CHOI
;
Ji Hyuk YANG
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine, Korea. tgjunsmc@gmail.com
- Publication Type:Case Report
- Keywords:
Heart neoplasms;
Rhabdomyoma;
Ventricular outflow tract obstruction, left;
Neonate
- MeSH:
Arrhythmias, Cardiac;
Echocardiography;
Follow-Up Studies;
Heart;
Heart Failure;
Heart Neoplasms;
Hemodynamics;
Humans;
Infant, Newborn;
Parturition;
Rhabdomyoma
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2010;43(6):725-728
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Rhabdomyoma is the most common benign cardiac neoplasm in neonates. Most patients with rhabdomyoma experienced spontaneous regression. Yet some of them need surgical therapy because of hemodynamic problems of the heart such as arrhythmia, outflow tract obstruction and valvular dysfunction. We found multiple masses in both ventricles on the patient's fetal echocardiogram. Heart failure caused by severe left ventricular outflow tract obstruction quickly presented after birth. The mass interfering with the outflow tract was resected via the transaortic approach at the first day of birth. Postoperative echocardiography showed complete release of the outflow tract obstruction. He was discharged on the postoperative day 8. During the 3 years of follow up, we found that the sizes of the remnant masses had gradually decreased.