A Case of Protein Losing Enteropathy Associated with Henoch-Schonlein Purpura.
- Author:
Kee Dae KIM
1
;
Chang Whan OH
;
Eun Young LEE
;
Jae Young KIM
Author Information
1. Department of Pediatrics, St. Benedict Hospital, Busan, Korea. jykim9@korea.com
- Publication Type:Case Report
- Keywords:
Henoch-Schonlein purpura;
Protein losing enteropathy
- MeSH:
alpha 1-Antitrypsin;
Antigen-Antibody Complex;
Arthritis;
Child;
Edema;
Female;
Glomerulonephritis;
Humans;
Hypoproteinemia;
Immunoglobulin A;
Protein-Losing Enteropathies*;
Purpura;
Purpura, Schoenlein-Henoch*
- From:Korean Journal of Pediatrics
2005;48(2):224-227
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Henoch-Schonlein purpura(HSP) is an IgA mediated immune complex vasculitic disease characterized by non-thrombocytic purpura, arthritis, gastrointestinal manifestations, and glomerulonephritis. HSP related glomerulonephritis induces hypoproteinemia and edema in some cases. Protein-losing enteropathy is another rare but known manifestation of HSP leading to hypoproteinemia and edema. We report a 6-year-old girl with HSP who showed edema caused by intestinal protein loss, evidenced by elevated fecal alpha 1 antitrypsin clearance.
