A Case of Atypical Teratoid/Rhabdoid Tumor Arising from the Supratentorial Area.
- Author:
Kyeong Hun JUNG
1
;
Young Se KWON
;
Yong Hun JUN
;
Soon Ki KIM
;
Young Jin HONG
;
Byong Kwan SON
;
Eun Young KIM
;
In Suh PARK
Author Information
1. Department of Pediatrics, College of Medicine, Inha University, Incheon, Korea. ysped@inha.ac.kr
- Publication Type:Case Report
- Keywords:
Atypical teratoid/rhabdoid tumor;
Supratentorium
- MeSH:
Central Nervous System;
Chemotherapy, Adjuvant;
Child;
Diagnosis;
Humans;
Incidence;
Microscopy
- From:Korean Journal of Pediatrics
2005;48(2):228-231
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Atypical teratoid/rhabdoid tumor may arise at any central nervous system location, but it is most commonly located in the cerebellum(60 percent). The incidence of this tumor remains unclear but it occurs most commonly in children less than 2 years of age. This highly malignant tumor shows a rapid progression and nonspecific radiologic findings. We report a case of primary intracranial atypical teratoid/rhabdoid tumor arising from the supratentorial area in early infancy. The diagnosis was made based on distinctive light microscopy and immunohistochemical findings. Despite aggressive surgical treatment with adjuvant chemotherapy, he died six months after his second operation.
