Two Cases of Cronkhite - Canada Syndrome with Remission.
- Author:
Hyo Jung KIM
1
;
Yoon Tae JEEN
;
Hoon Jai CHUN
;
Byung Won HUR
;
Young Sun KIM
;
Jae Hong PARK
;
Hwang Rae CHUN
;
Chang Don KANG
;
Jung Whan LEE
;
Chi Wook SONG
;
Soon Ho UM
;
Chang Duck KIM
;
Ho Sang RYU
;
Jin Hai HYUN
Author Information
1. Department of Internal Medicine, Institute of Digestive Disease and Nutrition, Korea University College of Medicine, Seoul, Korea.
- Publication Type:Original Article
- Keywords:
Cronkhite - Canada syndrome;
Intestinal polyposis;
Remission
- MeSH:
Adult;
Alopecia;
Canada*;
Diarrhea;
Ectoderm;
Humans;
Intestinal Polyposis;
Malnutrition;
Prognosis
- From:Korean Journal of Gastrointestinal Endoscopy
2000;21(1):543-548
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The Cronkhite-Canada Syndrome (CCS) is a monfamilial disorder of adults characterized by diffuse gastro-intestinal polyposis, ectodermal changes consisting of alopecia, dystrophy of nails and cutaneous hyper-pigmentation. The pathogenesis and the causes of CCS remain unknwon but the symptoms such as diarrhea and malnutrition are generally progressive, and the prognosis is knwon to be poor. Though the definitive treatment is not well known, it has been reported that the conservative management is the most important treatment, and that the clinical sourse can be reversible. One case was experienced involving Cronkhite-Canada Syndromen in a patient who was managed by conservative treatment and an other who was treated by corticosteroid. These two cases are reported herein with a review of corresponding literature.