Anesthetic Management of a Patient with Glanzmann's Thrombasthenia: A case report.
10.4097/kjae.2007.53.3.407
- Author:
Min Woo JEONG
1
;
Kwang Suk SEO
;
Hyun Jeong KIM
;
Kwang Won YUM
Author Information
1. Department of Anesthesiology and Pain Medicine, Seoul National University Hospital, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
dental procedure;
Glanzmann thrombasthenia;
platelet transfusion
- MeSH:
Anesthesia;
Blood Transfusion;
Child;
Factor VII;
Hemorrhage;
Humans;
Platelet Transfusion;
Thrombasthenia*
- From:Korean Journal of Anesthesiology
2007;53(3):407-410
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Glanzmann's thrombasthenia is a rare autosomal recessive disorder characterized by bleeding tendency due to decreased coagulation function of platelets. Perioperative adequate blood transfusion including preoperative platelet transfusion seems to be the most important component affecting anesthetic management. Also, minimally invasive techniques should be used at the time of induction of anesthesia and the use of recombinant activated coagulation factor VII may be considered. We successfully conducted an anesthetic management for dental procedure in a four-year-old child with Glanzmann's thrombasthenia using preoperative platelet transfusion. Thus we present this anesthetic experience and share informations on anesthetic management of patients with Glanzmann's thrombasthenia.