Chylothorax in Gorham's Disease.
10.3346/jkms.2002.17.6.826
- Author:
Won Sup LEE
1
;
Sung Han KIM
;
In Ho KIM
;
Hark Kyun KIM
;
Keun Seok LEE
;
Sang Yoon LEE
;
Dae Seog HEO
;
Bong Soon JANG
;
Yung Jue BANG
;
Noe Kyeong KIM
Author Information
1. Department of Internal Medicine, Seoul National University College of Medicine, Seoul, Korea. heo1013@plaza.snu.ac.kr
- Publication Type:Case Report
- Keywords:
Gorham's Disease;
Osteolysis;
Radiotherapy;
Pleurodesis;
Chylothorax
- MeSH:
Adult;
Chylothorax/complications/*pathology/radiotherapy;
Female;
Humans;
Magnetic Resonance Imaging/methods;
Osteolysis, Essential/complications/*pathology/*radiotherapy;
Pleurodesis;
Time Factors;
Tomography, X-Ray Computed;
Treatment Outcome
- From:Journal of Korean Medical Science
2002;17(6):826-829
- CountryRepublic of Korea
- Language:English
-
Abstract:
A 25-yr-old woman presented with a right pleural effusion. Destruction of 9th through 12th ribs, adjacent vertebral bodies, and transverse processes was noted on plain radiograph and a large low-attenuated, irregular shaped mass lesion with peripheral rim enhancement, destroying vertebral body and transverse process, was revealed on the computed tomographic scan. Magnetic resonance imaging showed high signal on T1- weighted image and iso- and low signal on T2-weighted image for the mass lesion replacing the vertebral bony cortex and marrow space. An open rib biopsy revealed the histopathological changes of Gorham's disease (essential osteolysis), even though only bloody fluid filling the empty space and rib and vertebral transverse process destruction were grossly observed on operation. Even though there was no definite response to radiotherapy and pleurodesis, the patient showed stable condition up to 20 months after diagnosis.
