A Case of Systemic Sclerosis in a Child.
- Author:
Ji Yeon CHANG
1
;
Ja Kyoung KIM
;
Jeong Hee KIM
;
Dae Hyun LIM
;
Byong Kwan SON
;
Jung Soo SONG
Author Information
1. Department of Pediatrics, College of Medicine, Inha University, Incheon, Korea. sonbk@inha.ac.kr
- Publication Type:Case Report
- Keywords:
Raynaud's phenomenon;
Systemic sclerosis
- MeSH:
Age of Onset;
Child*;
Connective Tissue Diseases;
Female;
Gastrointestinal Tract;
Heart;
Humans;
Lung;
Scleroderma, Systemic*;
Skin;
Subcutaneous Tissue
- From:Korean Journal of Pediatrics
2004;47(2):214-216
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Systemic sclerosis is a connective tissue disease involving primarily the skin and subcutaneous tissue but may involve other organ systems such as the lungs, gastrointestinal tract, and heart. Systemic sclerosis is a rare childhood disease. The age of onset for patients with systemic sclerosis has its peak between 30 and 50 years of age. Only 1 to 2% of all patients with systemic sclerosis have disease onset before the age of 10 years of age. We report a case of systemic sclerosis in a 7-year-old female who showed Raynaud's phenomenon as an initial manifestation.
