A Case of Febrile Ulceronecrotic Mucha-Habermann's Disease in an Infant.
- Author:
Soon Wook KWON
1
;
Jae Woo LIM
;
Moo Kyu SUH
;
Won Duck KIM
;
Tae Jung JANG
;
Bong Koo LEE
Author Information
1. Department of Dermatology, College of Medicine, Dongguk University, Korea. mksuhmd@hanmail.net
- Publication Type:Case Report
- Keywords:
Febrile ulceronecrotic Mucha-Habermann's disease;
Infant
- MeSH:
Diarrhea;
Fever;
Humans;
Infant*;
Liver Diseases;
Pityriasis Lichenoides;
Ulcer
- From:Korean Journal of Dermatology
2005;43(2):267-270
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Febrile ulceronecrotic Mucha-Habermann's disease (FUMHD) is an unusual severe form of pityriasis lichenoides et varioliformis acuta (PLEVA) characterized by abrupt onset of widespread ulceronecrotic cutaneous eruption associated with high fever and systemic symptoms. In most cases, a mild typical form of PLEVA was usually present prior to the acute fulminating course. We report a case of FUMHD in a 6-month-old infant, who presented widespread hemorrhagic papules and coalescent thickly crusted ulcerations, high fever, liver dysfunction, and diarrhea with histopathologic findings suggestive of PLEVA.