Bronchoscopic concerns in Proteus syndrome: a case report.
10.4097/kjae.2016.69.5.523
- Author:
Jung Min HONG
1
;
Hyeon Jeong LEE
;
Eun Soo KIM
;
Hae Kyu KIM
;
Soeun JEON
;
Hyae Jin KIM
Author Information
1. Department of Anesthesia and Pain Medicine, Pusan National University Hospital, Busan, Korea. lhjksk@pusan.ac.kr
- Publication Type:Case Report
- Keywords:
Difficult intubation;
Hamartomatous disorder;
Proteus syndrome
- MeSH:
Anesthesia;
Anesthesia, General;
Bronchoscopy;
Child;
Ear;
Facial Asymmetry;
Female;
Humans;
Intubation;
Neck;
Proteus Syndrome*;
Proteus*;
Scoliosis;
Tooth;
Torticollis
- From:Korean Journal of Anesthesiology
2016;69(5):523-526
- CountryRepublic of Korea
- Language:English
-
Abstract:
Proteus syndrome (PS) is a rare congenital hamartomatous disorder with multisystem involvement. PS shows highly clinical variability due to overgrowth of the affected areas, and several features can make anesthetic management challenging. Little is known about the airway problem associated with anesthesia in PS patients. An 11-year-old girl with PS was scheduled for ear surgery under general anesthesia. She had features complicating intubation including facial asymmetry and disproportion, abnormal teeth, limitation of neck movement due to torticollis, and thoracolumbar scoliosis. This study reports on a case of deformed airway of a PS patient under fiberoptic bronchoscopy.
