A Case of Job's Syndrome.
- Author:
Sung Joo LEE
1
;
Jeung LEE
;
Jeong Hun PARK
;
Joo Heung LEE
;
Sang Wahn KOO
;
Gwang Seong CHOI
;
Young Keun KIM
Author Information
1. Department of Dermatology, College of Medicine, Inha University, Inchon, Korea.
- Publication Type:Case Report
- Keywords:
Job's syndrome;
serum IgE level
- MeSH:
Abscess;
Chemotaxis;
Child;
Dermatitis;
Female;
Furunculosis;
Humans;
Immunoglobulin E;
Job Syndrome*;
Neutrophils;
Paronychia;
Pneumonia;
Pneumonia, Bacterial;
Staphylococcal Infections;
Tongue, Fissured
- From:Korean Journal of Dermatology
2000;38(10):1382-1384
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The Job's syndrome is a relatively rare primary immunodeficiency disorder characterized by recurrent staphylococcal infection and abscess formation, defective neutrophil chemotaxis, and markedly elevated serum IgE level. Clinical features are atopiclike dermatitis, furunculosis, paronychia, pulmonary bacterial pneumonia etc. We reported a case of Job's syndrome in a 12-year-old girl who had recurrent pneumonia, scaly pruritic dermatitis, fissured tongue, and nail dystrophy with elevated serum IgE level.
