Pulmonary Lymphangiomatosis.
10.4046/trd.1999.47.4.533
- Author:
Yong Seon CHO
1
;
Jee Hong YOO
;
Sang Yong SON
;
Hwoang Lae CHO
;
Soo Joong KIM
;
Min Soo HAN
;
Hong Mo KANG
Author Information
1. Department of Internal Medicine, College of Medicine, Kyung Hee University, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Pulmonary lymphangiomatosis;
Lymphangioleiomyomatosis;
Lymphatic system
- MeSH:
Adult;
Child;
Female;
Humans;
Infant;
Infant, Newborn;
Lymphangioleiomyomatosis;
Lymphatic System;
Pleura
- From:Tuberculosis and Respiratory Diseases
1999;47(4):533-537
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Pulmonary lymphangiomatosis is a very rare pulmonary lesion with an aggressive potential that occurs mainly in newborns, infants and young children of both sexes. It is characterized by pulmonary abnormalities of lymphatic system, showing an increased number of complex anastomosing lymphatic channels in the pleura, in the subpleural interlobular septa, and along the bronchovascular lymphatic route and uniformly fatal. We report a case of lymphangiomatosis behaving like lymphangioleiomyomatosis in a 26-year-old woman.
