Two cases of craniofacial dysostosis.
- Author:
Su Kyoung YU
1
;
Ki Hyun KANG
;
Kwang Joon KOH
Author Information
1. Department of Oral & Maxillofacial Radiology, School of Dentistry, and Institute of Oral Bio Science, Chonbuk National University, Korea. radkoh@chonbuk.ac.kr
- Publication Type:Case Report
- Keywords:
Craniofacial Dysostosis;
Facial Asymmetry
- MeSH:
Child, Preschool;
Congenital Abnormalities;
Cranial Sutures;
Craniofacial Dysostosis*;
Empyema;
Exophthalmos;
Facial Asymmetry;
Female;
Humans;
Hypertelorism;
Infant;
Intracranial Pressure;
Male;
Maxilla;
Sella Turcica;
Synostosis;
Tomography, X-Ray Computed
- From:Korean Journal of Oral and Maxillofacial Radiology
2004;34(3):165-169
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Craniofacial dysostosis is considered to be one of rarely observed syndromes characterized by premature closing of all cranial sutures. The first patient was a 4-year-old male infant who had been complaining of empyema. Clinical findings showed exophthalmos, hypertelorism and facial asymmetry. Conventional radiographs demonstrated abscence of cranial sutures and underdeveloped maxilla. CT scan demonstrated the digital impressions of the inner surface of the cranial vault, enlarged and depressed sella turcica. The second patient was a 2-year-old female infant who had been complaining of facial deformity. Clinical findings showed hypertelorism and underdeveloped maxilla. Radiographs showed premature synostosis of all cranial sutures, depressed and enlarged sella turcica, and hypoplastic maxilla. 3 years after operation, her look improved. However, resurgery may be considered to decreasing intracranial pressure and for correction of facial deformity. Two interesting cases showing 'cloverleaf'skulls were presented.
