Congenital Infantile Fibrosarcoma.
- Author:
Tae Hyoung KIM
1
;
Jae Hee CHUNG
;
Young Tack SONG
Author Information
1. Department of Surgery, College of Medicine, the Catholic University of Korea, Seoul, Korea. ytsong@catholic.ac.kr
- Publication Type:Case Report
- Keywords:
Infantile fibrosarcoma;
VAC chemotherapy
- MeSH:
Acute Kidney Injury;
Biopsy;
Dacarbazine;
Diagnosis;
Drug Therapy;
Emergencies;
Fibrosarcoma*;
Hemorrhage;
Humans;
Infant, Newborn;
Jejunum;
Magnetic Resonance Imaging;
Male;
Peritoneal Cavity;
Thigh;
Vital Signs
- From:Journal of the Korean Association of Pediatric Surgeons
2004;10(1):52-55
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A newborn male baby was transferred to our hospital with a left inguinal mass. The mass was huge measuring 10 x 10 cm, engorged, and dark-blue colored as a result of internal hemorrhage. Unstable vital signs were combined with DIC and acute renal failure. Emergency operation was performed because of the suspicion of bowel perforation. The peritoneal cavity was full of ascitis and the distal jejunum had a 0.5 cm perforation. Segmental resection of the jejunum and incisional biopsy of the inguinal mass were performed. On pelvic and thigh MRI, the mass protruded into pelvic cavity and encircled large vessels and nerves of the thigh. Pathologic diagnosis was congenital infantile fibrosarcoma. Fifteen days after operation, primary tumor excision was undertaken. The second look operation, performed after 6 times VAC chemotherapy, revealed no remained malignant cell on microscopic section. The baby has been followed closely for the last eight months.
