Tracheal Agenesis: A case report.
10.4097/kjae.1998.34.1.187
- Author:
Ji Yung LEE
1
;
Sang Youp KIM
;
Kyo Young LEE
;
Se Ho MOON
Author Information
1. Department of Anesthesiology, Catholic University Medical College, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Lung: respiratory distress syndrome;
tracheal agenesis;
tracheoesophageal fistula
- MeSH:
Autopsy;
Cyanosis;
Fistula;
Humans;
Infant, Newborn;
Intubation;
Thoracotomy;
Trachea;
Vocal Cords
- From:Korean Journal of Anesthesiology
1998;34(1):187-191
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Agenesis of trachea is a rare congenital anomaly. The main signs are respiratory distress, cyanosis, inability to vocalise and impossible tracheal intubation. There is no long-term surgical solution at present, therefore the condition is ultimately fatal. We report a case of tracheal agenesis. We anesthetized a 2.25 kg neonate for endoscopic examination, who was intubated successfully. Beyond 2.5 cm from the vocal cord, there was no trachea and we can only see esophageal lumen with fistula opening. After the endoscopic examination, exploratory thoracotomy was done, but surgical correction was impossible. After the surgery, she died from progressive ventilatory failure. Autopsy revealed a Floyd's type II tracheal agenesis with tracheo-esophageal fistula.
