A Case of Pancreatic Dual Wirsung Ducts in a Patient with von Hippel-Lindau Disease.
- Author:
Hye Soo KIM
1
;
Byung Hoon HAN
;
Sun Jung KIM
;
Jee Sook LEE
;
Sae Jin PARK
;
Sang Uk LEE
;
Bang HUR
;
Jung Hyun KIM
Author Information
1. Department of Internal Medicine, Kosin University College of Medicine, Busan, Korea. bhhankosin@hanmail.net
- Publication Type:Case Report
- Keywords:
von Hippel-Lindau disease;
Pancreas;
Pancreatic duct;
Dual Wirsung ducts
- MeSH:
Carcinoma, Renal Cell;
Cholangiopancreatography, Endoscopic Retrograde;
Humans;
Pancreas;
Pancreatic Ducts;
von Hippel-Lindau Disease
- From:Korean Journal of Gastrointestinal Endoscopy
2008;37(5):384-388
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Rare autosomal dominant disorders associated with various tumors and cysts, and several kinds of pancreatic lesions have been described in patients with von Hippel- Lindau (VHL) disease, but there have been few studies concerned with the variations of the pancreatic duct. We experienced a case of pancreatic dual Wirsung ducts in a patient with VHL disease. Computed tomography scans showed that multiple cysts had nearly completely replaced the pancreas, there was a solid tumor on the uncinate process of the pancreas and a left renal mass suggested renal cell carcinoma. ERCP shows that the Santorini duct and Wirsung duct were fused in a normal fashion, and another Wirsung duct had shrub-like branches that are commonly seen in pancreatic divisum.
