A Case of Epidermolysis Bullosa Herpetiformis.
- Author:
Bong Sung KIM
;
Dong Jin IM
;
Hye Sun YOON
;
Sung Jong PARK
;
Ki Soo KIM
;
Soo Young PI
;
Jai Kyoung KOH
;
EIIen A KIM
- Publication Type:Case Report
- Keywords:
Epidermolysis bullosa herpetiformis;
Intraepidermal blister
- MeSH:
Blister;
Diagnosis;
Epidermolysis Bullosa*;
Humans;
Infant, Newborn;
Parturition;
Skin
- From:Journal of the Korean Society of Neonatology
1997;4(2):253-259
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Epidermolysis bullosa (EB) is a rare inherited disease characterized by vesiculobullous lesion that arise in response to minimal trauma or shearing force to the skin. Epiderrnolysis bullosa herpetiformis-Dowling Meara, a variant of EB, has its onset at birth and can be a life threatening disease as it was in this case. We report a case of epidermolysis bullosa herpetiformis in a newborn with a generalized intraepidermal blisters noted at birth whose diagnosis was confirmed by electron microscope. A brief review of the literature is included.
