A Case of Epidermal Nevus Syndrome Associated with Urogenital Abnormalities.
10.5021/ad.1996.8.4.260
- Author:
Seog Jun HA
;
Sang Chin LEE
;
Si Yong KIM
;
Chung Won KIM
- Publication Type:Case Report
- Keywords:
Epidermal nevus syndrome;
Ovarian cyst and teratoma;
Solitary kidney
- MeSH:
Adolescent;
Extremities;
Female;
Humans;
Kidney;
Nevus*;
Ovarian Cysts;
Ovary;
Teratoma;
Tomography, X-Ray Computed;
Urogenital Abnormalities*
- From:Annals of Dermatology
1996;8(4):260-264
- CountryRepublic of Korea
- Language:English
-
Abstract:
The epidermal nevus syndrome is a disorder characterized by epidermal nevi and associated neurologic, skeletal, and other abnormalities. A 15-year-old female patient presented with extensive, bilateral systematized, verrucous plaques, involving the face, trunk, both extremities, and anogenital area. The onset of the lesions were at the age of 2 months. Abdominal CT showed the absence of the left kidney, teratoma of the right ovary and left ovarian cyst. This is a case of epidermal nevus syndrome, which was composed of extensive epidermal nevi, congenital solitary kidney, left ovarian cyst and right ovarian teratoma.
