A Case of Klippel-Trenaunay-Weber Syndrome Presenting with Esophageal and Gastric Varices Bleeding.
- Author:
Ji Hoon KIM
1
;
Chang Whan KIM
;
Dong Kyun SON
;
Byung Wha CHUNG
;
Seong Eun YANG
;
Jin Il KIM
;
Jae Kwang KIM
;
In Sik CHUNG
Author Information
1. Department of Internal Medicine, The Catholic University of Korea College of Medicine, Seoul, Korea. jkkim@cmc.cuk.ac.kr
- Publication Type:Case Report ; English Abstract
- Keywords:
Klippel-Trenaunay-Weber syndrome;
Hemangioma;
Hypertension;
portal;
Esophageal and Gastric Varices
- MeSH:
Adult;
English Abstract;
Esophageal and Gastric Varices/*complications;
Gastrointestinal Hemorrhage/*etiology;
Humans;
Hypertension, Portal/complications;
Klippel-Trenaunay-Weber Syndrome/*complications;
Male;
Portal Vein/abnormalities
- From:The Korean Journal of Gastroenterology
2004;43(2):137-141
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Klippel-Trenaunay-Weber syndrome is a congenital vascular disorder consisted of a variety of vascular malformations, enlargement of the involved limb, and varicose veins. We report a case of Klippel-Trenaunay-Weber syndrome presenting portal hypertension and varices bleeding caused by hypoplasia of the portal vein. Portal hypertension was caused by portal vein hypoplasia associated with Klippel-Trenaunay-Weber syndrome. There were three episodes of variceal bleeding, and hemostasis were achieved by endoscopic band ligation, Sugiura operation, and splenic artery embolization respectively. Although successful hemostasis was achieved, an additional procedures to reduce portal hypertension were needed to prevent repeated episodes of variceal bleeding.
