A Case of Primary Rhabdomyosarcoma in the Left Cerebello-Pontine Angle.
- Author:
Sung Bo SHIM
1
;
Yong Moon JUN
;
Yung Chul OK
;
Kyu Woong LEE
;
Jeong Rae KIM
;
Moon Hyang PARK
Author Information
1. Department of Neurosurgery, National Medical Center, Korea.
- Publication Type:Original Article
- MeSH:
Adult;
Autopsy;
Brain;
Cerebellopontine Angle;
Cerebellum;
Child;
Diagnosis;
Female;
Humans;
Radiotherapy;
Rhabdomyosarcoma*
- From:Journal of Korean Neurosurgical Society
1977;6(1):215-220
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The primary rhabdomyosarcoma of the brain is very rare. There are only 14 cases reported in the literatures till 1975, and the majority of them were arised in the cerebellum. The intracranial rhabdomyosarcomas may be originated from the multipotent mesenchymal cells of aberrent muscle tissue in the leptomeninges. The histological 3 types are adult pleomorphic, alveolar and embryonal type. The demonstration of cross-striation is confirmed for diagnosis of this tumor. All of these tumors tend to have a short clinical course, but the survival time seems to be slightly improved by surgical excision followed by radiotherapy. We have recently experienced one case of primary rhabdomyosarcoma in the left cerebellopontine angle of 9 year-old girl, which was confirmed by operation and complete autopsy.
