Progressive Moyamoya Syndrome Associated with Paroxysmal Nocturnal Hemoglobinuria.
- Author:
Sung Geun RYU
1
;
Se Jin LEE
Author Information
1. Department of Neurology, Yeungnam University College of Medicine, Daegu, Korea. sejinmayo@ynu.ac.kr
- Publication Type:Case Report
- Keywords:
Moyamoya syndrome;
Paroxysmal nocturnal hemoglobinuria;
Progression
- MeSH:
Adult;
Carotid Artery, Internal;
Cerebral Infarction;
Constriction, Pathologic;
Female;
Hemoglobinuria, Paroxysmal*;
Humans;
Infarction;
Magnetic Resonance Imaging;
Moyamoya Disease*;
Paresis;
Posterior Cerebral Artery
- From:Journal of the Korean Neurological Association
2014;32(4):285-288
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A 31-year-old female with paroxysmal nocturnal hemoglobinuria (PNH) presented with left hemiparesis. One year prior to this presentation she had been diagnosed with bihemispheric cerebral infarctions associated with moyamoya syndrome. During her current presentation, MRI revealed acute infarction of the right hemisphere and MRA revealed occlusion of the right internal carotid artery (ICA), and aggravation of the preexisting stenosis of the contralateral ICA and ipsilateral posterior cerebral artery compared to the previous MRA. We report herein a case of progressive moyamoya syndrome associated with PNH.
