A Case of Kennedy Syndrome Mimicking Myasthenia Gravis.
- Author:
Byung Ju LEE
1
;
Ki Han KWON
;
Sung Min KIM
;
Ha Ry NA
;
Byung Chul LEE
;
Sang Hyo RYU
;
Jae Chun BAE
;
Jee In KIM
;
Jin Sung LEE
Author Information
1. Department of Neurology, Hallym University College of Medicine.
- Publication Type:Case Report
- Keywords:
Kennedy syndrome;
Decremental response;
Anticholinesterase
- MeSH:
Amyotrophic Lateral Sclerosis;
Bulbo-Spinal Atrophy, X-Linked*;
Cholinesterase Inhibitors;
Humans;
Myasthenia Gravis*
- From:Journal of the Korean Neurological Association
2001;19(5):544-546
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Patients with Kennedy syndrome, which progresses more slowly than amyotrophic lateral sclerosis show a mild degree of motor fluctuation but rarely show significant decremental responses to repetitive nerve stimulations. Even in a patient with decremental responses to repetitive nerve stimulations, there is usually no significant improvements in motor symptoms to anticholinesterases. We experienced a patient with Kennedy syndrome, who showed significant decremental responses to repetitive nerve stimulations and a marked degree of motor fluctuation. His motor fluctuation responded dramatically to anticholinesterase. (J Korean Neurol Assoc 19(5):544~546, 2001)
