Paratesticular Alveolar Rhabdomyosarcoma with Multiple Lymph Nodes Metastasis Successfully Treated with Chemotherapy.
10.12701/yujm.2011.28.1.70
- Author:
Ha young LEE
1
;
Myung Soo HYUN
;
Kyung Hee LEE
;
Min Kyoung KIM
;
Sung Ae KOH
;
Se Hoon SOHN
;
Sung Woo PARK
;
Dong Geun KIM
;
Myung Jin KIM
;
Hyo Jin JANG
;
Mi Jin KIM
Author Information
1. Department of Internal Medicine, College of Medicine, Yeungnam University, Daegu, Republic of Korea. hms@med.yu.ac.kr
- Publication Type:Case Report
- Keywords:
Rhabdomyosarcoma;
Alveolar;
Lymphatic Metastasis
- MeSH:
Adolescent;
Adult;
Arm;
Child;
Dactinomycin;
Extremities;
Humans;
Lymph Nodes;
Lymphatic Metastasis;
Neoplasm Metastasis;
Prognosis;
Rhabdomyosarcoma;
Rhabdomyosarcoma, Alveolar;
Young Adult
- From:Yeungnam University Journal of Medicine
2011;28(1):70-76
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Rhabdomyosarcomas are soft tissue sarcomas; while extremely rare in adults, they are one of the most common neoplasms in children and adolescents. Histologically, they can be classified into embryonal(ERMS), alveolar(ARMS), pleomorphic, and undifferentiated types. The ARMS type is very rare, and is associated with a poor prognosis. Common primary sites of ARMS are the trunk and extremities. We report on a case of paraaortic, supraclavicular, and axillary lymph node metastasis from paratesticular ARMS treated with VAC(vincristine, dactinomycin, cyclophosphamide)/ IE(ifosfamide, etoposide) chemotherapy in a young adult. Administration of six cycles of chemotherapy with VAC/ IE resulted in complete remission. The patient has maintained complete remission over the past 27 months.
