A Case of Childhood Dermatofibrosarcoma Protuberans.
- Author:
Kwang Soo KIM
;
Hwan Gyo JEONG
;
Jong Min KIM
;
Cheol Heon LEE
;
Se Heum JOH
- Publication Type:Case Report
- Keywords:
Childhood;
Dermatofibrosarcoma protuberans
- MeSH:
Child;
Dermatofibrosarcoma*;
Dermis;
Extremities;
Fibroblasts;
Humans;
Male;
Parturition
- From:Korean Journal of Dermatology
1989;27(4):474-476
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Dermatofibrosarcoma protuberans(DFSP) is a rare, distinctive cutsneous tumor originating in the dermis that appears as a raised uninodular or multinodular lesion on the trunk or the proximal extremities. In about 10% of the cases, DFSP arises in childhood and it is rarely evident already at birth. Histopathologically, DFSP shows the chsracteristic storiform and cartwheel patterns, with the fibroblasts arranged radially about a small central hub of fibrous tissue. We report herein a case of childhood DFSP in a 7-year-old boy.
