- Author:
Philip Judson M. de la Vega
1
;
Madonna Victoria S. Calderon-Domingo
1
Author Information
- Publication Type:Case Reports
- MeSH: Human; Female; Adult: 25-44 yrs old; mullerian failure; mullerian aplasia; adenomyosis; pelvin pain
- From: Philippine Journal of Reproductive Endocrinology and Infertility 2025;22(1):7-15
- CountryPhilippines
- Language:English
- Abstract: In Mayer-Rokitansky-K0ster-Hauser (MRKH) syndrome, the development of the uterus and some parts of the vagina is either completely absent or reduced. It is a rare congenital anomaly, and affects one in 4,000-5,000 female births and commonly presents as primary amenorrhea. Approximately 6% - 10% of these patients with MRKH syndrome report persistent pelvic pain, which may be attributed to the presence of myomas, endometriosis, adenomyosis or hematometra caused by a functioning endometrial tissue in a uterine remnant. This paper presents the case of a 37 year old nulligravid who experienced severe cyclic hypogastric pain, and was subsequently diagnosed with MRKH syndrome with adenomyosis. Clinical evaluation and definitive management of the index case are discussed.
- Full text:2025092123160309184pjrei 22(1) CReport 2.pdf