Chinese expert consensus on surgical treatment of congenital heart disease: Unilateral absence of a pulmonary artery
- VernacularTitle:先天性心脏病外科治疗中国专家共识：单侧肺动脉缺如
- Author:
Wenlei LI
1
;
Li MA
1
;
Shusheng WEN
2
,
3
;
Xinxin CHEN
1
;
Shoujun LI
4
,
5
;
Jinghao ZHENG
6
Author Information
1. 1. Heart Center, Guangzhou Women and Children s Medical Center, Guangzhou Medical University, Guangdong Provincial Clinical Research Center for Child Health, Guangzhou, 510180, P. R. China
2. Guangdong Cardiovascular Institute, Guangdong Provincial People'
3. s Hospital, Guangdong Academy of Medical Sciences, Guangzhou Medical University, Guangzhou, 510180, P. R. China
4. Chinese Academy of Medical Sciences &
5. Peking Union Medical College National Center for Cardiovascular Diseases, Fuwai Hospital Pediatric Surgery Center, Beijing, 100037, P. R. China
6. Department of Cardiothoracic Surgery, Shanghai Children s Medical Center, School of Medicine, Shanghai Jiao Tong University, National Children s Medical Center, Shanghai, 200127, P. R. China
- Publication Type:Journal Article
- Keywords:
Unilateral absence of a pulmonary artery;
congenital heart disease;
surgical treatment;
expert consensus
- From:
Chinese Journal of Clinical Thoracic and Cardiovascular Surgery
2025;32(07):905-908
- CountryChina
- Language:Chinese
-
Abstract:
Unilateral absence of a pulmonary artery (UAPA) is a rare congenital malformation resulting from the failed development or premature involution of the sixth aortic arch during embryogenesis, leading to a failure to establish a connection with the main pulmonary artery. Currently, there is a notable lack of consensus regarding the surgical management of UAPA in China. Drawing upon the latest clinical research, this consensus aims to summarize surgical approaches and techniques to improve the clinical management of UAPA patients and serve as a scientific reference for physicians specializing in pediatric cardiology and structural heart disease. This consensus aims to promote the standardization of UAPA diagnosis and treatment, thereby facilitating improved patient outcomes and long-term management, and stimulating the continuous development and innovation of surgical treatment for this condition in China.
