A case of lymphangioleiomyomatosis that presented with recurrent pneumothorax in a postmenopausal woman.
- Author:
Gun Min PARK
1
;
Hyun Jee KIM
;
Jin Young OH
;
Hyun Ju LEE
;
Sung Goo HAN
;
Joo Hyun KIM
;
Young Soo SHIM
Author Information
1. Department of Internal Medicine and Lung Institute, Seoul National University College of Medicine, Seoul, Korea. hansk@snu.ac.kr
- Publication Type:Case Report
- Keywords:
Lymphangioleiomyomatosis;
Menopause;
Pneumothorax
- MeSH:
Diagnosis;
Diffusion;
Dyspnea;
Female;
Humans;
Korea;
Lung;
Lymphangioleiomyomatosis*;
Menopause;
Pathology;
Pneumothorax*;
Rare Diseases
- From:Korean Journal of Medicine
2007;72(1):90-94
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Lymphangioleiomyomatosis is a rare disease which mostly occurs during the reproductive ages of premenopausal women. The presenting symptoms of lymphangioleiomyomatosis include cystic lung lesions, progressive dyspnea on exertion, and recurrent pneumothorax. HRCT shows bilateral diffusely scattered tiny cysts and PFT shows obstructive airflow limitation and decreased diffusion capacity. We report a case of lymphangioleiomyomatosis which presented with recurrent pneumothorax and characteristic cysts in HRCT. The diagnosis was confirmed by pathology. This is the first case of lymphangioleiomyomatosis diagnosed for a postmenopausal woman in Korea. Lymphangioleiomyomatosis must be considered in the diagnosis for a postmenopausal woman with characteristic symptoms and radiologic findings for Korean patients.
