Basal cell nevus syndrome: 2 case reports.
- Author:
Jae Duk KIM
1
;
Yo Seob SEO
;
Jin Soo KIM
Author Information
1. Department of Oral & Maxillofacial Radiology, College of Dentistry, Chosun University, Gwangju, Korea. hidds@chosun.ac.kr
- Publication Type:Case Report
- Keywords:
Jaw cysts;
Basal cell nevus syndrome;
Tooth, Impacted
- MeSH:
Basal Cell Nevus Syndrome;
Follow-Up Studies;
Jaw Cysts;
Nevus;
Odontogenic Cysts;
Ribs;
Tooth, Impacted
- From:Korean Journal of Oral and Maxillofacial Radiology
2008;38(2):109-115
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The basal cell nevus syndrome (BCNS) is an autosomal dominant disorder, characterized by basal cell carcinomas, odontogenic keratocysts and skeletal abnormalities. We experienced two cases that represented several characteristics of BCNS. Case 1: a thirty three year-old man visited CSU hospital. His radiographs showed four cystic lesions at both maxillary sinus and both mandibular angle, with bifid rib and ectopic calcification of falx cerebri. After marsupialization and enucleation, recurrent and newly developing tendency were found on his follow-up radiographs. Case 2: a seventeen year-old man had four large cystic lesions which were diagnosed as odontogenic keratocysts. He had craniofacial anomalies which included ectopic calcification and frontal bossing.
