A Case of Hybrid Surgery for Left Subclavian Artery Aneurysm Concomitant with Loeys-Dietz Syndrome in Childfood
- VernacularTitle:小児期に発症したロイス・ディーツ症候群合併の左鎖骨下動脈瘤症例に対するハイブリッド手術の1例
- Author:
Masahiro RYUGO
1
;
Osamu MONTA
1
;
Noriyuki KASHIYAMA
1
;
Shusaku MAEDA
2
;
Hiroki NAKATSUJI
3
;
Yasushi TSUTSUMI
1
Author Information
- Keywords: Loeys-Dietz syndrome; left subclavian artery aneurysm; hybrid surgery
- From:Japanese Journal of Cardiovascular Surgery 2025;54(2):91-94
- CountryJapan
- Language:ja
- Abstract: We report on a rare case of a left subclavian artery aneurysm concomitant with Loeys-Dietz Syndrome (LDS) which required us to operate in childhood. A 12-year-old female, who had been diagnosed with LDS by genetic examination one year eariler, was revealed to be suffering from a left subclavian artery aneurysm (25 mm in diameter) by follow up chest MRI scan. Hybrid surgery consisting of coil embolization of aneurysm and surgical revascularization of the left subclavian artery and left vertebral artery was performed successfully. The patient was discharged on postoperative day 8.