Monosegmental Hepatobiliary Fibropolycystic Disease Mimicking a Mass: Report of Three Cases.
- Author:
Jung Hyeok KWON
1
;
Mi Jeong KIM
;
Young Hwan KIM
;
Koo Jeong KANG
;
Yu Na KANG
;
Sun Young KWON
Author Information
- Publication Type:Case Reports
- Keywords: Ductal plate malformations; Fibropolycystic disease; Monosegmental disease; Caroli disease
- MeSH: Adult; Bile Duct Diseases/*diagnosis; Cysts/*diagnosis; Diagnostic Imaging/methods; Female; Fibrosis/diagnosis; Gallbladder Diseases/diagnosis; Humans; Liver Cirrhosis/diagnosis; Liver Diseases/*diagnosis; Liver Neoplasms/diagnosis; Male
- From:Korean Journal of Radiology 2014;15(1):54-60
- CountryRepublic of Korea
- Language:English
- Abstract: Hepatobiliary fibropolycystic diseases are a unique group of entities involving the liver and biliary tract, which are caused by abnormal embryologic development of the ductal plates at various stages. We experienced strange hepatobiliary fibropolycystic diseases with a complex mass composed of malformed ducts and biliary cysts, which did not belong to, and were different from, previously known malformations. They were unique in imaging and histologic features. We herein report three cases of monosegmental hepatobiliary fibropolycystic disease mimicking a mass.
